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Scimitar Syndrome Variant with Hypersensitivity Pneumonitis

Imaging findings

Hypoplastic right lung, partial anomalous pulmonary venous return (PAPVR) with partial left atrial connection, and mosaic attenuation from hypersensitivity pneumonitis.

Key takeaways

Scimitar syndrome variants can involve complex venous drainage patterns that may be incidentally discovered during workup for other conditions like hypersensitivity pneumonitis.

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