CTICasesAzygos Continuation of the Inferior Vena Cava with Polysplenia and Intestinal Malrotation
Imaging findings
Chest radiograph shows a prominent right paratracheal stripe representing a dilated azygos vein. Abdominal and thoracic CT confirms the absence of the intrahepatic segment of the inferior vena cava with azygos continuation, polysplenia (multiple small spleens with independent vascular supplies), and intestinal malrotation, with the colon located on the left and the small bowel on the right.
Key takeaways
Azygos continuation of the IVC is a congenital anomaly frequently associated with heterotaxy syndromes, particularly left isomerism (polysplenia syndrome). These patients may also exhibit intestinal malrotation and other congenital anomalies, which are often discovered incidentally in adulthood.
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