Granulomatosis with Polyangiitis (GPA) with Splenic Involvement
Imaging findings
Large, circumscribed, ill-defined apical lung opacities with patent vessels/airways, progressing to extensive cavitation and necrosis. Notable concurrent finding of substantial splenic ischemia/infarction.
Key takeaways
GPA should be considered in cases of rapidly progressive cavitary lung disease. Splenic involvement, while rare, is a recognized manifestation of systemic vasculitis.
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