Pulmonary Vein Atresia (Secondary Lymphangiectasia)
Imaging findings
Septal edema, amorphous mediastinal tissue, and systemic arterial hypertrophy; definitive diagnosis found via angiogram showing absent right pulmonary veins.
Key takeaways
Chronic congestion from venous anomalies can mimic primary lymphoproliferative disorders like lymphangiomatosis.
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