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Pulmonary Vein Atresia (Secondary Lymphangiectasia)

Imaging findings

Septal edema, amorphous mediastinal tissue, and systemic arterial hypertrophy; definitive diagnosis found via angiogram showing absent right pulmonary veins.

Key takeaways

Chronic congestion from venous anomalies can mimic primary lymphoproliferative disorders like lymphangiomatosis.

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