Anomalous Right Coronary Artery with Coronary Artery Fistula to Right Ventricle
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
Coronary CT angiography showed an enlarged left main coronary artery. The right coronary artery ostium was absent. Following the left main coronary artery and proximal left anterior descending artery, an anomalous artery branched off, taking a sharp right turn with a pre-pulmonic course, identified as the right coronary artery. This anomalous right coronary artery then looped around, displayed a small aneurysm, and demonstrated a distinct 'puff of contrast' emptying directly into the right ventricle.
Key takeaways
This case illustrates a complex combination of congenital coronary anomalies: an anomalous origin of the right coronary artery from the left main coronary artery with a pre-pulmonic course, coupled with a large coronary artery fistula draining into the right ventricle. The enlarged left main coronary artery and patient's symptoms are explained by the fistula, which creates a 'steal phenomenon' due to significant shunting. These congenital variants, even if present from birth, can manifest clinically with symptoms later in life.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Renal Cell Carcinoma with Lymphangitic CarcinomatosisNeoplastic
- Miliary TuberculosisInfection
- Presumed Kawasaki Disease with Coronary AneurysmsVascular
- Calcified Mediastinal/Pericardial Mass (Old Hematoma)Inflammatory
- Massive Mediastinal LiposarcomaNeoplastic
- Interstitial Lung Edema with Lymphatic PearlsVascular
- Mucus in Airways Simulating Parenchymal Nodules (MIPS Pitfall)Artifact
- Extralobar Sequestration with Phrenic Nerve InvolvementCongenital
See all cases from July 10, 2015 →
Related Congenital cases
- Hyper-IgE Syndrome (Job's Syndrome) with Bronchiectasis
- Hybrid Congenital Pulmonary Airway Malformation (CPAM) and Pulmonary Sequestration
- Ostial Atresia of the Coronary Sinus
- Congenitally Corrected Transposition of the Great Arteries (ccTGA) with Ventricular Septal Defect
- Bronchial Atresia with Bronchocele and CPAM Features
- Venous-Lymphatic Malformation with Hemangioma Features and Incidental Carcinoid Tumorlet