Kartagener Syndrome
Imaging findings
CT chest shows complete situs inversus (right-sided heart and left-sided liver/spleen), associated with severe, chronic bronchiectasis, mucus plugging, and mosaic perfusion representing small airway disease (bronchiolitis obliterans).
Key takeaways
Kartagener syndrome is a subset of primary ciliary dyskinesia characterized by the triad of situs inversus, chronic sinusitis, and bronchiectasis. The impaired ciliary clearance leads to recurrent respiratory tract infections, chronic airway inflammation, and progressive bronchiectasis.
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