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Congenital Absent Pericardium

Congenital Absent Pericardium▶ Watch on YouTube — age-restricted, cannot embed here

Imaging findings

On radiograph, the heart's apex is lifted and appears more laterally located, suggesting levo rotation. CT images confirm levo rotation of the heart and show a thin wisp of pericardial tissue in one area, but no visible pericardium elsewhere.

Key takeaways

Congenital absence of the pericardium is a rare anomaly, more commonly involving the left pericardium. It results from early regression of the anterior superior cardinal vein during embryological development. This condition typically causes malrotation of the heart. While often asymptomatic, a small pericardial defect can lead to cardiac herniation, which can be a significant problem.

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