Congenital Absent Pericardium
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
On radiograph, the heart's apex is lifted and appears more laterally located, suggesting levo rotation. CT images confirm levo rotation of the heart and show a thin wisp of pericardial tissue in one area, but no visible pericardium elsewhere.
Key takeaways
Congenital absence of the pericardium is a rare anomaly, more commonly involving the left pericardium. It results from early regression of the anterior superior cardinal vein during embryological development. This condition typically causes malrotation of the heart. While often asymptomatic, a small pericardial defect can lead to cardiac herniation, which can be a significant problem.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Pulmonary Veno-Occlusive Disease (PVOD) secondary to Systemic SclerosisAutoimmune
- Pulmonary Capillary Hemangiomatosis (PCH)Vascular
- Calcified Pleuralith (Pleural Mouse)Metabolic
- Pulmonary Artery Aneurysm in Beckwith-Wiedemann SyndromeCongenital
- Iatrogenic Tension Pneumothorax due to Malpositioned Heimlich ValveIatrogenic
- Juxtaposed Atrial AppendagesCongenital
- Recurrent Strongyloides Infection (Migratory Eosinophilic Pneumonia)Infection
- Strongyloides Hyperinfection Syndrome with Pneumocystis PneumoniaInfection
See all cases from May 19, 2016 →