CTICasesPulmonary Veno-Occlusive Disease (PVOD) secondary to Systemic Sclerosis
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Imaging findings
The patient presents with dense lungs showing ground-glass opacities and septal thickening, alongside peripheral ground-glass opacities. Imaging reveals a large pulmonary artery, a dilated and thickened right ventricle and right atrium, a small pericardial effusion, some pleural effusion, and lymphadenopathy, with a relatively small left atrium.
Key takeaways
Pulmonary Veno-Occlusive Disease (PVOD) is a known complication of collagen vascular diseases like systemic sclerosis. Key imaging findings that help differentiate PVOD from primary pulmonary arterial hypertension (PAH) include septal thickening, a small left atrium (due to diminished blood flow), and lymphadenopathy, especially in a patient with elevated pulmonary pressures but a normal pulmonary artery wedge pressure. Vasodilators should be avoided in these patients.
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