CTICasesLoeys-Dietz Syndrome with Vessel Tortuosity
Imaging findings
In a 27-year-old patient with Loeys-Dietz syndrome, there is extreme 'corkscrew-like' appearance of the tortuous splenic artery. A previous patient with the syndrome also showed enormous tortuosity of the vertebral and internal carotid arteries. The patient's aortic arch also has a somewhat high and abnormal appearance.
Key takeaways
Loeys-Dietz syndrome is a connective tissue disease causing early aortic dissection and aneurysm of the aortic root and ascending aorta. It also causes significant vessel tortuosity (e.g., vertebral, internal carotid, and splenic arteries), which may have prognostic implications. Radiologists should specifically look for vessel tortuosity in these patients.
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