CTICasesSpontaneous Pneumothorax in Marfan Syndrome
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Imaging findings
CT shows a dilated aortic root, typical of Marfan syndrome, along with a sizable pneumothorax and apical bullae or blebs in both lungs. Post-drainage radiograph also demonstrates these apical bullae.
Key takeaways
Pneumothorax due to ruptured apical bullae is a known pulmonary manifestation of Marfan syndrome, and should be considered in Marfan patients presenting with chest pain, even if aortic dissection is suspected.
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