CTICasesPulmonary Hamartoma with Congenital Unilateral Pulmonary Artery Agenesis
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Imaging findings
Chest radiographs and CT demonstrate a hypoplastic, structurally abnormal right lung with significant rightward mediastinal shift. The right pulmonary artery is completely absent (proximal interruption), and there are no identifiable right pulmonary veins. Multiple transpleural systemic arterial collaterals are present. Within the hypoplastic right lung, a slowly growing, lobulated nodule containing coarse calcification is observed.
Key takeaways
Congenital unilateral absence (proximal interruption) of a pulmonary artery is a rare anomaly that results in a hypoplastic lung supplied solely by systemic collaterals and abnormal bronchial branching patterns. Co-existing nodules like a pulmonary hamartoma, while benign, may grow and mimic carcinoid tumors or lung cancers in young patients, prompting surgical resection such as a wedge resection.
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