Congenital Lung Anomaly with Tracheal Stenosis (Probable Complete Tracheal Rings)
Imaging findings
The initial chest radiograph showed right-sided volume loss and increased lucency, but CT disproved Scimitar syndrome or Swyer-James. CT revealed a single-lobe right lung with an aberrant bronchial branching pattern and no true fissures. Critically, the trachea was notably large at the thoracic inlet but uniformly narrowed throughout its intrathoracic course to the carina, highly suggestive of complete tracheal rings. Spinal segmentation anomalies and a rudimentary right superior pulmonary vein were also present.
Key takeaways
This complex congenital case demonstrates multiple associated anomalies, including a single-lobed lung and probable complete tracheal rings, which were the likely cause of the patient's long-standing dyspnea and exercise intolerance, underscoring the importance of evaluating all thoracic structures.
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