Isolated Systemic Arterial Supply to the Lung
Imaging findings
Chest CT and subsequent catheter angiography demonstrate a large, tortuous, calcified anomalous systemic artery arising from the upper abdominal aorta and supplying normal lung tissue in the right lower lobe. The lobe lacks any sequestration-like soft tissue mass, and the airways and bronchi are normal. Drainage occurs normally via the inferior pulmonary vein.
Key takeaways
Isolated systemic arterial supply to the lung (pseudo-sequestration) is a rare congenital anomaly where a portion of normal lung is supplied by a systemic artery rather than a pulmonary artery. Due to high systemic pressures, these anomalous vessels can develop early atherosclerotic changes, calcification, aneurysmal dilatation, or rarely rupture and dissection, often warranting elective endovascular coil embolization.
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