CTICasesPlexiform Arteriopathy in Idiopathic Pulmonary Arterial Hypertension
Imaging findings
Chest radiographs show enlargement of the main and right interlobar pulmonary arteries, cardiomegaly, and a central venous catheter. Chest computed tomography and maximum intensity projection reconstructions demonstrate sudden caliber changes in the small pulmonary arterioles with tiny dot-like aneurysms and surrounding focal, smudgy ground glass opacities.
Key takeaways
In patients with severe idiopathic pulmonary arterial hypertension, sudden nodular or dot-like arteriolar enlargements surrounded by ground glass halos represent plexiform lesions. It is important to distinguish these findings from other causes of diffuse ground glass opacities, such as pulmonary capillary hemangiomatosis or pulmonary veno-occlusive disease.
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