CTICasesTruncus Arteriosus Type II with Quadricuspid Pulmonic Valve
Imaging findings
CT demonstrates a single arterial trunk arising from the ventricles with the left and right pulmonary arteries arising separately from the posterior and posterolateral aspects of the ascending trunk, consistent with type II truncus arteriosus (pulmonary arteries arising from posterior lateral walls of the common trunk). Additionally, the pulmonic valve is quadricuspid rather than the usual tricuspid or bicuspid configuration. A large atrial septal defect is also present.
Key takeaways
Truncus arteriosus is a conotruncal malformation in which a single arterial vessel arises from the heart and gives rise to the aorta, pulmonary artery, and coronary arteries. Type II truncus has the left and right pulmonary arteries arising from the posterior or posterolateral wall of the common trunk rather than as a common trunk (type I) or from the aorta separately (type III). The coincident finding of a quadricuspid valve, while an extremely rare anomaly on its own, illustrates the spectrum of conotruncal and valvular abnormalities that can co-occur.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- NUT Carcinoma (Midline NUT Carcinoma)Neoplastic
- Bronchial Artery Origin Mimicking Aortic Intimal InjuryArtifact
- Bilateral Foramen of Morgagni HerniasCongenital
- Right Atrial Myxoma with OssificationNeoplastic
- Congenital Bronchial AtresiaCongenital
- Loeys-Dietz Syndrome with Pectus CarinatumCongenital
- Mycobacterium Avium Complex (MAC) Infection Misidentified as SilicosisInfection
- Hypersensitivity Pneumonitis Progressing to FibrosisILD
See all cases from September 21, 2017 →
Related Congenital cases
- Large Right Upper Lobe Pulmonary Vein with Mass Effect on Bronchus Intermedius
- Dual Left Anterior Descending Artery (Dual LAD) Coronary Variant
- Pulmonary Artery Sling Incidentally Discovered on Lung Cancer Screening CT
- Congenital Systemic-to-Pulmonary Artery Fistula — Internal Mammary Artery to Left PA
- Complex Pleuropulmonary Lymphatic-Venous Malformation
- Right Aortic Arch with Mirror-Image Branching and Right Ligamentum Arteriosum