CTICasesPrimary Ciliary Dyskinesia (Kartagener Syndrome) with Situs Inversus and Bronchiectasis
Imaging findings
Chest radiograph and CT show situs inversus (heart and abdominal viscera reversed) together with extensive bronchiectasis -- bubbly, chain-like dilated airways -- more pronounced in the lower lobes, with mucus/debris impaction filling some of the larger airways; the patient has a known ciliary motility disorder.
Key takeaways
The triad of situs inversus, bronchiectasis, and chronic sinopulmonary disease defines Kartagener syndrome, a subtype of primary ciliary dyskinesia; the eponym is more accurately pronounced with a hard "g" ("Kartagener"), reflecting Dr. Kartagener's Germanic rather than French background, contrary to a popular but likely apocryphal conference anecdote.
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