Juvenile chronic arthritis-associated interstitial lung disease
[...]. Juvenile chronic arthritis-associated interstitial lung disease. CTICases. Published August 31, 2018. https://cticases.com/c/p9yku
Imaging findings
Serial chest CT scans over 16 years starting in early childhood show progressive lower lobe volume loss, reticulation, traction bronchiectasis, and esophageal dilatation, alongside scattered, thin-walled perivascular pulmonary cysts and centrilobular emphysema-like lucencies, in a young non-smoking woman with juvenile chronic arthritis.
Key takeaways
Juvenile chronic arthritis can rarely cause progressive interstitial lung disease in children and young adults. The imaging presentation is often a mixed pattern, containing features of non-specific interstitial pneumonia (basilar-predominant fibrosis) and lymphocytic interstitial pneumonia (cysts).
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