CTICasesScimitar Syndrome with Right Upper Lobe Drainage and Probable Accessory Hemidiaphragm
Imaging findings
Imaging confirmed Scimitar syndrome with a Scimitar vein draining into the IVC. Unusually, this anomalous vein drained an abnormal right upper lobe, rather than the more typical right lower lobe. The right lung also demonstrated volume loss and mediastinal shift, with abnormal airway branching. A soft tissue band extending into the lung, possibly an accessory hemidiaphragm, was also noted.
Key takeaways
An intriguing variant of Scimitar syndrome characterized by drainage of the right upper lobe by the anomalous vein, accompanied by other congenital anomalies such as abnormal lung lobation and a possible accessory hemidiaphragm.
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