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Partial Anomalous Pulmonary Venous Return (PAPVR) with Sinus Venosus ASD

Imaging findings

Radiographs show cardiomegaly and marked dilatation of the pulmonary arteries and veins. CT confirms the absence of a normal left superior pulmonary vein draining into the left atrium. Instead, there is a sinus venosus atrial septal defect associated with partial anomalous pulmonary venous return, where anomalous pulmonary veins from the right upper lobe drain directly into the superior vena cava.

Key takeaways

Partial anomalous pulmonary venous return of the right upper lobe is highly associated with a superior sinus venosus atrial septal defect. The chronic left-to-right shunt results in volume overload, pulmonary overcirculation, and eventually severe pulmonary arterial hypertension. Corrective surgery typically involves a Warden procedure, which reroutes the anomalous pulmonary venous return back to the left atrium.

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