Mounier-Kuhn Syndrome
Imaging findings
Chest CT shows marked dilatation of the trachea (transverse diameter >3 cm) and main bronchi, with severe cystic bronchiectasis and lower lobe panlobular emphysema.
Key takeaways
Mounier-Kuhn syndrome (tracheobronchomegaly) is a rare congenital disorder characterized by marked dilation of the trachea and main bronchi due to atrophy of elastic fibers and smooth muscle, often associated with severe bronchiectasis.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Duodenal Bobby Pin Perforation and Liver AbscessTrauma
- Necrotizing Pneumonia with Pseudoaneurysm RuptureInfection
- Superinfected Bronchogenic CystCongenital
- Disseminated Bartonella henselaeInfection
- Giant Pleural Plaques Simulating Horseshoe LungExposure
- Subpleural Curvilinear Lines in AsbestosisExposure
- Coronary PeriarteritisAutoimmune
- Inferior Sinus Venosus Atrial Septal DefectCongenital
See all cases from March 22, 2019 →