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Mounier-Kuhn Syndrome

Imaging findings

Chest CT shows marked dilatation of the trachea (transverse diameter >3 cm) and main bronchi, with severe cystic bronchiectasis and lower lobe panlobular emphysema.

Key takeaways

Mounier-Kuhn syndrome (tracheobronchomegaly) is a rare congenital disorder characterized by marked dilation of the trachea and main bronchi due to atrophy of elastic fibers and smooth muscle, often associated with severe bronchiectasis.

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