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Kartagener Syndrome

Imaging findings

Chest radiograph and CT show situs inversus totalis (left-sided liver, right-sided stomach/heart) and severe lower-lobe predominant cystic bronchiectasis, mucus plugging, and extensive mosaic attenuation/air trapping.

Key takeaways

Kartagener syndrome is a triad of situs inversus, chronic sinusitis, and bronchiectasis, representing a form of primary ciliary dyskinesia. The lung disease is characterized by chronic infections, bronchiectasis, and marked expiratory air trapping.

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