Kartagener Syndrome
Imaging findings
Chest radiograph in a patient post-bilateral lung transplantation demonstrates situs inversus totalis, including dextrocardia, a right-sided aortic arch, a left-sided SVC, and a right-sided gastric bubble. Following transplant, a right minor fissure is present on the right (corresponding to the donor's right lung), whereas the patient pre-operatively had a left minor fissure.
Key takeaways
Kartagener syndrome (primary ciliary dyskinesia with situs inversus totalis) leads to bronchiectasis and chronic lung failure, frequently necessitating lung transplantation. Because of the chest wall and vascular inversion, surgeons must anastomose the donor's right lung to the native left chest and vice versa, which is anatomically challenging but routinely performed. Post-transplant radiographs reflect the donor's normal lung anatomy in the inverted chest cavity.
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