Hemangiomatosis (Likely Left-Sided)
Imaging findings
A mediastinal mass showing arterial supply from chest wall vessels was noted, with associated lower mediastinal and abdominal components. Multiple phleboliths were present within the tissue. The condition appeared predominantly left-sided, involving the mediastinum, left back muscles, left kidney, and peritesticular tissue (after left testicular hemangioma resection), but without liver lesions.
Key takeaways
Hemangiomatosis involves multiple hemangiomas, which are benign vascular tumors often containing phleboliths. This condition can present with multisystem involvement, and in rare cases, may exhibit a striking unilateral or segmental distribution (mosaicism), suggesting an underlying genetic predisposition or somatic mutation. Such cases may prompt consideration of Proteus syndrome, although this patient did not have visible deformities.
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