Congenital Airway and Vascular Anomalies with Morgagni Hernia
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
Chest radiography shows a large anterior-inferior mediastinal mass that CT reveals to be a large, fat-containing Morgagni hernia. Multiplanar CT reconstructions also demonstrate a constellation of congenital airway and vascular anomalies: a small, aborted tracheal bronchus; diffuse, severe intrathoracic tracheal stenosis suggestive of complete tracheal rings; absent right main bronchus with the right upper lobe bronchus and bronchus intermedius arising directly from the distal trachea; a duplicated left brachiocephalic vein draining into the coronary sinus; and a single right pulmonary vein.
Key takeaways
Congenital airway anomalies, such as tracheal stenosis with complete rings, bronchial branching variations, and tracheal bronchi, are frequently associated with concurrent vascular and venous anomalies. Patients with these complex abnormalities can remain completely asymptomatic into adulthood, with the lesions discovered incidentally during imaging for unrelated issues, such as a trauma or a Morgagni hernia.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Congenital Right Coronary Artery Aneurysm with Fistulization to the Coronary SinusCongenital
- Iatrogenic Superior Vena Cava RuptureIatrogenic
- Pulmonary Pneumocystis jirovecii Pneumonia and Cerebral Lymphoproliferative Disorder in HIVInfection
- Thymoma Associated with Pure Red Cell AplasiaNeoplastic
- Amiodarone-Induced Pulmonary ToxicityILD
- Chronic Pulmonary Thromboembolism with Pulmonary Infarction and CavitationVascular
- Endobronchial Metastasis from MelanomaNeoplastic
- Constrictive Pericarditis, Fibrothorax, and Iatrogenic Left Atrial Cannulation by Chest TubeIatrogenic
See all cases from January 22, 2015 →
Related Congenital cases
- Anomalous Retrovascular Left Upper Lobe Bronchus
- Birt-Hogg-Dubé Syndrome
- Obstructed Supracardiac TAPVR and Heterotaxy Syndrome with Asplenia
- Esophageal Duplication Cyst Extending Through Diaphragm
- Proximal Interruption of the Right Pulmonary Artery and Thymic Carcinoma
- Anomalous Right Coronary Artery with Myocardial Bridging