CTICasesCongenital Pulmonary Airway Malformation Type 1
Imaging findings
CT chest in a patient in their 20s shows a large, multicystic abnormality containing large, clean-looking cystic spaces in the left lower lobe, pushing the left major fissure and lingula anteriorly and superiorly, without surrounding parenchymal scarring.
Key takeaways
Congenital pulmonary airway malformation (CPAM, formerly CCAM) Type 1 is characterized by one or more large cysts (typically >2 cm) in a single lobe. While often diagnosed prenatally or in infancy, mild cases can present in young adults. Resection is generally recommended due to the risks of recurrent infection and a small risk of malignant transformation into mucinous adenocarcinoma.
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