CTICasesScimitar Syndrome with Pseudo-Horseshoe Lung
Imaging findings
Chest CT and MR imaging demonstrate an anomalous right pulmonary vein draining into the inferior vena cava, consistent with a scimitar vein. A portion of the right lung posterolaterally herniates across the midline behind the heart. Associated findings include an abnormal right mainstem bronchial branching pattern and a ventricular septal defect.
Key takeaways
Scimitar syndrome is a congenital anomaly characterized by anomalous pulmonary venous return from the right lung to the IVC, frequently associated with right lung hypoplasia and systemic arterial supply to the right lung. A known association is the 'pseudo-horseshoe' lung, where a portion of the right lung posterolaterally herniates across the midline behind the heart. This should be distinguished from true congenital horseshoe lung, which involves actual parenchymal fusion across the midline and carries a much poorer prognosis.
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