CTICasesCongenital Pulmonary Airway Malformation and Bronchial Atresia Hybrid Lesion
Imaging findings
Chest CT in a young adult smoker presenting with a pneumothorax shows a localized region of highly disorganized, cystic lung within the left upper lobe, with fluid- and debris-filled central bronchi that do not connect to the left main bronchus. The surrounding lung tissue is relatively normal, suggesting a hybrid congenital thoracic lesion with features of both bronchial atresia and congenital pulmonary airway malformation (CPAM), potentially exacerbated by smoking-related emphysema.
Key takeaways
Hybrid congenital pulmonary malformations can present in young adulthood with complex features of both bronchial atresia and CPAM. These lesions may first manifest clinically due to complications such as a pneumothorax or superimposed emphysematous changes.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Mitral Valve Abscess and VegetationInfection
- Transfusion-Related Hepatosplenic and Lymph Node HemosiderosisMetabolic
- Unicuspid Aortic Valve and Aortic AneurysmCongenital
- Esophageal HemangiomaNeoplastic
- Pacemaker Lead Dislodgement into the Inferior Vena Cava Post-ResuscitationIatrogenic
- Macklin Phenomenon and Acute Lung Injury from Cocaine and Methamphetamine AbuseExposure
- Tracheobronchial and Parenchymal AmyloidosisMetabolic
- Diffuse Idiopathic Pulmonary Neuroendocrine Cell HyperplasiaNeoplastic
See all cases from November 30, 2016 →
Related Congenital cases
- Complete Inferior Accessory Fissure with Aberrant Bronchial Supply
- Giant Muscular Ventricular Septal Defect (VSD) with Dual-Chamber Right Ventricle
- Lymphangiomatosis with Dystrophic Calcification
- Systemic Arterial Supply with Hypoplastic Right Lung
- Eisenmenger Syndrome
- Superior Sinus Venosus ASD and PAPVR