Mounier-Kuhn Syndrome
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Imaging findings
Chest radiography and CT demonstrate marked dilatation of the trachea and mainstem bronchi, with mixed bronchiectasis predominantly in the right lower lobe, peribronchial thickening, patchy ground-glass opacities, and air trapping on expiratory imaging.
Key takeaways
Mounier-Kuhn syndrome, or tracheobronchomegaly, is characterized by marked dilatation of the tracheobronchial tree. While often congenital due to elastic fiber deficiency, it can also be acquired or exacerbated by chronic lung injury, such as bronchopulmonary dysplasia secondary to prolonged neonatal positive-pressure ventilation.
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