CTICasesNeurofibromatosis with Ruptured Intercostal Artery Aneurysms
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Imaging findings
Portable film shows abnormal soft tissue overlying the arch and subtle subcutaneous nodules. Gated CT confirms subcutaneous nodules (associated with neurofibromatosis) and reveals large aneurysms arising from intercostal arteries, some of which had ruptured. Angiography confirms intercostal artery aneurysms.
Key takeaways
Intercostal artery aneurysms are a rare complication of neurofibromatosis and can rupture, leading to major bleeding requiring thoracic surgery. There's an old name, von Recklinghausen vasculopathy, though not commonly used.
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