CTICasesPrimary Pulmonary Artery Sarcoma
Imaging findings
CT demonstrates a large, expanding soft tissue mass filling the main pulmonary artery and extending across the midline into both the right and left lobar and segmental pulmonary arteries, with vessels coursing through the mass. It does not look like chronic thromboembolic pulmonary hypertension (CTEPH) due to the expanding soft tissue component extending to the pulmonic valve.
Key takeaways
Primary pulmonary artery sarcoma is a rare, highly malignant tumor arising from the intima of the pulmonary trunk. It frequently mimics chronic pulmonary embolism or CTEPH, leading to delayed diagnosis. Differentiating features on CT/MRI include expansion of the pulmonary artery lumen, direct invasion of the vessel wall/midline crossing, and heterogeneous contrast enhancement of the intraluminal mass.
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