CTICasesErdheim-Chester disease
Imaging findings
Chest CT shows soft tissue infiltration surrounding the descending aorta and perinephric space. PET CT demonstrates intense FDG uptake in the posterior orbits bilaterally (retrobulbar infiltration), whereas the aortic and perinephric fibrotic lesions show minimal metabolic activity.
Key takeaways
Erdheim-Chester disease can involve multiple compartments, including the orbits where retrobulbar macrophage infiltration causes exophthalmos. PET CT is helpful to map disease activity, as chronic fibrotic lesions may be metabolically inactive.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Pulmonary embolismVascular
- Innominate artery stenosisVascular
- Small cell lung carcinomaNeoplastic
- Typical carcinoidNeoplastic
- Smoking-related diffuse lung diseaseExposure
- Juvenile chronic arthritis-associated interstitial lung diseaseILD
- Aortopulmonary windowCongenital
- Pulmonary vein smoke artifactArtifact
See all cases from August 31, 2018 →