CTICasesErdheim-Chester Disease
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Imaging findings
A 58-year-old male presented with a right atrial mass mimicking liposarcoma. MRI showed a diffuse infiltrative process involving the right atrial epicardium. Systemic imaging demonstrated additional infiltrative soft tissue in the posterior mediastinum and bilateral renal involvement, highly suggestive of Erdheim-Chester disease.
Key takeaways
Erdheim-Chester disease is a multisystem histiocytic neoplasm that can manifest as infiltrative soft tissue processes in the mediastinum, epicardium, and retroperitoneum (kidneys). It should be considered in the differential diagnosis for epicardial or mediastinal soft tissue infiltration, particularly when systemic involvement is present.
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