CTICasesLymphangiomatosis (Gorham-Stout Syndrome Spectrum)
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Imaging findings
Serial chest radiographs over several years showed chronic, progressive, unilateral (right lower lobe) interstitial opacities. CT revealed soft tissue thickening along central bronchovascular structures and septal lines in the right lower lobe, with pleural thickening, a small chronic effusion, and small, uncalcified mediastinal lymph nodes. Lytic bone lesions were also present at multiple levels.
Key takeaways
Persistent unilateral interstitial opacities should raise suspicion for lymphatic obstruction or infiltration. In the context of associated lytic bone lesions, consider lymphatic malformation syndromes such as lymphangiomatosis or Gorham-Stout syndrome. These conditions involve proliferation of lymphatic channels that can cause pleural effusions, interstitial thickening, and osteolysis.
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