CTICasesProgressive Cystic Lung Disease and Bronchiectasis in Sjögren Syndrome
Imaging findings
Severe and progressively worsening cystic lung disease and bronchiectasis are evident by dilated, thin-walled bronchi and extensive cystic changes asymmetrically distributed throughout the lungs. There are also findings of remote upper lobe tuberculosis.
Key takeaways
Sjögren syndrome, often associated with systemic lupus erythematosus, can lead to severe and progressive cystic lung disease and bronchiectasis, distinct from interstitial pneumonias. The diagnosis relies on clinical features (dry eyes/mouth) and serology (SSA/SSB antibodies), with biopsies showing lymphocytic infiltration.
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