CTICasesTuberous Sclerosis Complex with Lymphangioleiomyomatosis (LAM) and Multifocal Micronodular Pneumocyte Hyperplasia (MMPH)
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Imaging findings
CT of the chest in a 34-year-old female reveals a right-sided pneumothorax treated with a chest tube, alongside numerous, uniformly distributed, thin-walled lung cysts characteristic of lymphangioleiomyomatosis. Additionally, there are scattered small, ground-glass nodules representing multifocal micronodular pneumocyte hyperplasia, myocardial fatty foci, and multiple low-attenuation renal angiomyolipomas.
Key takeaways
Lymphangioleiomyomatosis is a progressive cystic lung disease that can present with spontaneous pneumothorax and is frequently associated with tuberous sclerosis complex. Key ancillary findings of tuberous sclerosis on chest CT include multifocal micronodular pneumocyte hyperplasia, myocardial fatty foci, and renal angiomyolipomas.
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