CTICasesBronchiectasis with Thin Bronchial Walls (Possible Williams-Campbell Syndrome or Sjogren's Phenotype)
Imaging findings
CT demonstrates dramatic, widespread bronchiectasis, characterized by conspicuously dilated bronchi with remarkably thin or imperceptible walls, contrasting with the typical thickened, inflamed walls seen in other forms of bronchiectasis. Some cystic changes are also present in conjunction with the dilated airways.
Key takeaways
This case presents an unusual form of bronchiectasis characterized by very thin bronchial walls, raising the differential diagnosis of Williams-Campbell syndrome (due to cartilage deficiency) or a specific manifestation in Sjogren's syndrome, as suggested by similar cases observed by the presenter. The absence of thickened inflamed walls is a key distinguishing feature, and it highlights the challenge of pathological confirmation in adults.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Sarcoidosis Presenting as Emphysema in a Non-SmokerAutoimmune
- Large Coronary Artery Fistula from RCA to Right Atrium (Follow-up)Congenital
- Meandering Pulmonary Vein with Anomalous Connection to Right Innominate VeinCongenital
- Anomalous Left Main Coronary Artery Arising from RCA with Fistula to Coronary SinusCongenital
- Systemic-to-Pulmonary Venous Collaterals Secondary to Severe Pulmonary HypertensionVascular
- Adenocarcinoma in the Context of Fibrosing Lung DisorderNeoplastic
- Displaced Tongue Ring in the EsophagusIatrogenic
- Sjogren's Syndrome with Cystic Lung Disease and BronchiectasisAutoimmune
See all cases from September 9, 2016 →
Related Congenital cases
- RCA Sinoatrial Nodal Branch Fistula Draining to Right Atrium
- Bicuspid Pulmonic Valve with Main Pulmonary Artery Enlargement
- Absent Right Superior Vena Cava with Left Superior Vena Cava Draining to Coronary Sinus
- Infected Esophageal Duplication Cyst with Communication
- Left Lung Agenesis with Right Lung Extension into Left Hemithorax
- Aortic Coarctation with Sinus Venosus Atrial Septal Defect and Anomalous Pulmonary Venous Drainage