CTICasesSjogren's Syndrome with Cystic Lung Disease and Bronchiectasis
Imaging findings
This patient with known Sjogren's syndrome exhibits cystic spaces and bronchiectasis, with some foci that may represent lymphoid hyperplasia. While bronchi are dilated, many areas show inflamed, thickened bronchial walls, which helps distinguish it from the prior case of thin-walled bronchiectasis. Amorphous calcified material is also noted.
Key takeaways
This case illustrates lung manifestations of Sjogren's syndrome, including cystic lung disease and bronchiectasis. The presence of inflamed, thickened bronchial walls helps differentiate it from conditions like Williams-Campbell syndrome, despite some shared features of bronchial dilatation. The discussion also touches on possible elastolysis from protein deposition (amyloid) as a mechanism for cystic changes.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Sarcoidosis Presenting as Emphysema in a Non-SmokerAutoimmune
- Large Coronary Artery Fistula from RCA to Right Atrium (Follow-up)Congenital
- Meandering Pulmonary Vein with Anomalous Connection to Right Innominate VeinCongenital
- Anomalous Left Main Coronary Artery Arising from RCA with Fistula to Coronary SinusCongenital
- Systemic-to-Pulmonary Venous Collaterals Secondary to Severe Pulmonary HypertensionVascular
- Adenocarcinoma in the Context of Fibrosing Lung DisorderNeoplastic
- Displaced Tongue Ring in the EsophagusIatrogenic
- Bronchiectasis with Thin Bronchial Walls (Possible Williams-Campbell Syndrome or Sjogren's Phenotype)Congenital
See all cases from September 9, 2016 →
Related Autoimmune cases
- Kawasaki Disease with Coronary Aneurysms and Occlusions
- Constrictive Bronchiolitis in Rheumatoid Arthritis with Complicating Invasive Aspergillosis
- Severe Granulomatosis with Polyangiitis (GPA) with Airway and Sinus Involvement
- Progressive Cystic Lung Disease and Bronchiectasis in Sjögren Syndrome
- Diaphragmatic Atrophy and Fatty Replacement in Polymyositis
- Sarcoidosis with Pseudo-Plaque Pattern