CTICasesDouble Aortic Arch with Complete Vascular Ring
Imaging findings
In an 8-day-old with airway and esophageal symptoms, CT shows a right aortic arch descending on the right with a diverticulum-like outpouching and apparent mirror-image branching; the anterior branching vessel arises more from the side than from the top of the arch, and there is a focal atretic segment within the diverticulum.
Key takeaways
An anterior arch branch that arises laterally from the side of the arch rather than from its superior aspect, combined with a diverticulum containing an atretic segment, favors a double aortic arch with an atretic left arch component over a simple right aortic arch with aberrant left subclavian artery; a double aortic arch forms a complete, though sometimes clinically silent, vascular ring and typically occurs in isolation without associated congenital heart disease.
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