CTICasesUnexplained Bronchiectasis, Cystic Lung Disease, and Recurrent Pneumothoraces
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Imaging findings
A 16-year-old presented with bullous lesions, upper lobe predominant bronchiectasis, cystic spaces (some fluid-filled), and striking mosaic attenuation. Over a decade, the patient experienced recurrent pneumothoraces, presumably from rupture of peripheral bullae/blebs. Workup for cystic fibrosis and Williams-Campbell syndrome was negative.
Key takeaways
This complex case of progressive bronchiectasis and cystic lung disease with recurrent pneumothoraces, despite negative workup for common causes like cystic fibrosis, suggests an unusual underlying condition such as an atypical connective tissue disorder, immune deficiency, or severe bronchiolitis obliterans.
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