CTICasesPolysplenia Syndrome with Left Isomerism and Azygos Continuation
Imaging findings
CT shows bilateral hyparterial bronchi (bilateral left-sided isomerism) and absence of the hepatic segment of the inferior vena cava with azygos continuation, visible on radiographs as a subtle paraspinous interface and a dilated azygos vein.
Key takeaways
Left lung isomerism (polysplenia syndrome) is a congenital anomaly characterized by bilateral hyparterial bronchi (bilateral "left" lungs) and is strongly associated with azygos continuation of the inferior vena cava. The dilated azygos vein can be identified on frontal radiographs as a right paratracheal mass or a prominent paraspinous interface.
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