CTICasesCombined PVOD and PCH in Scleroderma
Imaging findings
CT chest in a scleroderma patient with severe pulmonary arterial hypertension shows diffuse ground-glass opacity, centrilobular ground-glass micronodules, vascular tortuosity in the lower lobes, and fluid in the fissures/interstitial edema.
Key takeaways
Pulmonary veno-occlusive disease (PVOD) and pulmonary capillary hemangiomatosis (PCH) are rare, related causes of pulmonary hypertension that can occur in connective tissue diseases like scleroderma. Key CT findings include centrilobular ground-glass nodules, smooth septal thickening, and pleural effusion, representing post-capillary obstruction.
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