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Atypical Granulomatosis with Polyangiitis

Imaging findings

CT chest shows a bilateral bronchiolitis/bronchopneumonia pattern characterized by centrilobular tree-in-bud opacities and patchy ground-glass areas. Biopsy confirmed multifocal vasculitis and vaguely granulomatous inflammation of vessels consistent with GPA.

Key takeaways

Granulomatosis with polyangiitis (GPA) classically presents with large cavitary nodules or masses. However, atypical presentations can mimic infectious bronchopneumonia or bronchiolitis, with centrilobular tree-in-bud opacities representing peribronchial vasculitis, requiring correlation with ANCA serology.

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