Atypical Granulomatosis with Polyangiitis
Imaging findings
CT chest shows a bilateral bronchiolitis/bronchopneumonia pattern characterized by centrilobular tree-in-bud opacities and patchy ground-glass areas. Biopsy confirmed multifocal vasculitis and vaguely granulomatous inflammation of vessels consistent with GPA.
Key takeaways
Granulomatosis with polyangiitis (GPA) classically presents with large cavitary nodules or masses. However, atypical presentations can mimic infectious bronchopneumonia or bronchiolitis, with centrilobular tree-in-bud opacities representing peribronchial vasculitis, requiring correlation with ANCA serology.
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