CTICasesPulmonary Veno-Occlusive Disease
Imaging findings
V/Q scan shows multiple unmatched segmental perfusion defects with normal ventilation, mimicking chronic thromboembolic pulmonary hypertension (CTEPH). Contrast-enhanced chest CT shows right ventricular dilatation, severe bilateral interlobular septal thickening, peribronchovascular soft-tissue infiltration/edema, and normal-caliber pulmonary veins. Right heart catheterization confirms severe pulmonary hypertension (systolic PAP 110 mmHg).
Key takeaways
Pulmonary veno-occlusive disease (PVOD) is a rare, progressive vascular disorder characterized by fibrous occlusion of the pulmonary venules. It is a well-known mimic of CTEPH on V/Q scans. Key CT findings that differentiate PVOD from other causes of pulmonary hypertension include diffuse septal lines, ground-glass centrilobular nodules, and mediastinal/hilar lymphadenopathy in the setting of severe pulmonary hypertension and normal left atrial pressure.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Ollier DiseaseCongenital
- Gold Thread AcupunctureIatrogenic
- Pulmonary Tumor EmbolismNeoplastic
- Iatrogenic Circumflex Artery OcclusionIatrogenic
- Pulmonary SlingCongenital
- Mitral-Aortic Intervalvular Fibrosa PseudoaneurysmInfection
- Retained Acupuncture NeedlesIatrogenic
- CoccidioidomycosisInfection
See all cases from December 8, 2017 →