CTICasesSarcoidosis-related Pulmonary Vein Stenosis and Pulmonary Hypertension
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
A 2013 CT scan reveals bulky, confluent mediastinal and hilar lymphadenopathy associated with obstructive features. Multiple pulmonary veins show stenoses, including the right inferior, right superior, and branches of the left pulmonary veins, with associated post-stenotic dilation. Subsequent imaging after stenting of the pulmonary veins demonstrates persistent in-stent stenosis in some vessels and diminished flow in others, indicating ongoing compromise.
Key takeaways
Sarcoidosis can cause severe pulmonary hypertension through various mechanisms, including extrinsic compression or direct infiltration leading to pulmonary vein stenosis. This central venous obstruction leads to severe pulmonary hypertension, which is challenging to manage. Stenting may be attempted but can be complicated by in-stent stenosis or lack of sustained patency.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Organizing Pneumonia Triggered by Radiation TherapyInflammatory
- Pacemaker Lead Complications (Shredded/Stuck Lead and Broken Lead Fragment)Iatrogenic
- Right Hemidiaphragmatic Dysfunction Post Atrial AblationIatrogenic
- Miliary Coccidioidomycosis in AIDS PatientInfection
- Necrotic Adenocarcinoma Mimicking Lung AbscessNeoplastic
- Diffuse Pulmonary Calcifications in Alveolar Septal AmyloidosisMetabolic
- Mammary Fibromatosis (Desmoid Tumor) Post Breast Implant SurgeryNeoplastic
- Esophageal Submucosal Metastasis from Breast CancerNeoplastic
See all cases from June 12, 2015 →
Related Autoimmune cases
- Pulmonary Eosinophilic Infiltration (Hyper-eosinophilic Syndrome / Eosinophilic Granulomatosis with Polyangiitis)
- Sarcoidosis with Airway Compression and Air Trapping
- Bruton's Agammaglobulinemia with Chronic Bronchial Disease
- Tracheobronchomalacia with Airway Calcifications in a Cartilaginous Inflammatory Disease
- Acute Lupus Pneumonitis and Serositis
- Dermatomyositis with Organizing Pneumonia and Non-Specific Interstitial Pneumonia