CTICasesCongenitally Corrected Transposition of the Great Arteries (ccTGA) with Ventricular Septal Defect
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
Chest CT reveals an abnormal configuration of the great vessels, with the ascending aorta positioned anteriorly and to the left, and the pulmonary artery positioned posteriorly and to the right (L-transposition). There is also ventricular-arterial and atrioventricular discordance, a large outlet ventricular septal defect (VSD), and severe enlargement of the main pulmonary artery branches.
Key takeaways
Congenitally corrected transposition of the great arteries (ccTGA or L-TGA) is characterized by double discordance, where the morphologic right ventricle supports the systemic circulation and the morphologic left ventricle supports the pulmonary circulation. While many patients survive into adulthood without surgery, they are at high risk for systemic right ventricular failure, tricuspid regurgitation (often termed "left Ebstein's anomaly"), and progressive pulmonary hypertension, especially when associated with a large ventricular septal defect.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Severe Three-Vessel Coronary Artery Disease with Myocardial HibernationVascular
- Voriconazole-Induced PeriostitisInflammatory
- Retained Surgical Sponge (Gossypiboma)Iatrogenic
- Lymphomatoid Granulomatosis (Grade 3)Neoplastic
- Hyper-IgE Syndrome (Job's Syndrome) with BronchiectasisCongenital
- Bronchial AnthracofibrosisExposure
- Syphilitic AortitisInfection
- Neglected Basal Cell Carcinoma of the Chest WallNeoplastic
See all cases from July 8, 2015 →
Related Congenital cases
- Bronchial Atresia with Bronchocele and CPAM Features
- Venous-Lymphatic Malformation with Hemangioma Features and Incidental Carcinoid Tumorlet
- Congenital Hyaline Membrane Deficiency / Large Bullous Emphysema
- Thrombosed Lateral Tunnel Fontan Palliation
- Bronchogenic Cyst with Congenital Absence of Right Upper Lobe Bronchus and Single Right Pulmonary Vein
- Bicuspid Aortic Valve Aortopathy (Left-Right Fusion Pattern)