CTICasesCOPA Syndrome
Imaging findings
Chest CT in a 20-year-old female with a history of Still's disease and macrophage activation syndrome shows diffuse pulmonary hyperattenuation (cysts and ground glass) and persistent, chronic axillary and mediastinal lymphadenopathy.
Key takeaways
COPA (coatomer subunit alpha) syndrome is a rare autosomal dominant autoimmune disease. It classically presents with a combination of inflammatory arthritis (often misdiagnosed as juvenile idiopathic arthritis or Still's disease) and cystic/fibrotic interstitial lung disease.
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Extra-Lumenal Displacement of SVC Dialysis CatheterIatrogenic
- Iatrogenic Subclavian Artery CannulationIatrogenic
- Intralobar Bronchopulmonary Sequestration with Premature AtherosclerosisCongenital
- Recanalized Pulmonary AVM with Transpleural CollateralsCongenital
- In-Situ Thrombus in Methamphetamine-Induced Pulmonary HypertensionVascular
- Flail Posterior Mitral Valve LeafletVascular
- Young-Onset Pleuroparenchymal FibroelastosisILD
- Scedosporium Apiospermum Infection in Neutropenic AMLInfection
See all cases from July 23, 2020 →