CTICasesYoung-Onset Pleuroparenchymal Fibroelastosis
Imaging findings
CT in a 21-year-old male shows progressive bilateral upper lobe subpleural consolidation, marked pleural thickening, and superior retraction of the hila. The patient also presented with profound sensorineural hearing loss.
Key takeaways
Pleuroparenchymal fibroelastosis (PPFE) is a rare interstitial lung disease characterized by pleural and subpleural alveolar wall elastosis. While typically seen in older adults, it can present in young adults (early 20s), sometimes showing unusual associations like sensorineural hearing loss.
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