CTICasesComplex Congenital Anomalies: Right Aortic Arch with Aberrant Innominate Artery, Total Anomalous Pulmonary Venous Return of Left Lung, and Cor Triatriatum Sinister
▶ Watch on YouTube — age-restricted, cannot embed here
Imaging findings
Diverticulum of Kommerell, an aberrant innominate artery giving rise to both the left subclavian and left carotid arteries, originating from a right-sided aortic arch with a tight stenosis between the subclavian and carotid. Total anomalous pulmonary venous return of the entire left lung, draining into the systemic circulation. Additionally, a septum in the left atrium partially divides the right-sided pulmonary veins from the rest of the left atrium, consistent with cor triatriatum sinister. Marked narrowing and probable bronchomalacia of the left lower lobe bronchus are also noted.
Key takeaways
This case presents a remarkable combination of multiple, previously undiagnosed congenital anomalies, including complex aortic arch variations, total anomalous pulmonary venous return, and cor triatriatum sinister. The presence of such extensive developmental insults can lead to other systemic issues like scoliosis and severe hemodynamic consequences such as a large left-to-right shunt (elevated Qp:Qs).
AI-assisted summary — may contain errors. Verify against the source video. Learn more
More from this webinar
- Williams Syndrome with Supravalvular Aortic Stenosis and Pulmonary Artery NarrowingCongenital
- Alveolar Capillary Dysplasia with Unroofed Coronary Sinus (Right-to-Left Shunt)Congenital
- Iatrogenic Esophageal Rupture from Blakemore Tube PlacementIatrogenic
- Primum Atrial Septal Defect (ASD)Congenital
- Pulmonary Alveolar MicrolithiasisMetabolic
- Esophageal Varices Anastomosing with an Inferior Pulmonary VeinVascular
- Unroofed Coronary Sinus (Isolated Finding)Congenital
- Unilateral Perched Facet at C7-T1 with ParaplegiaTrauma
See all cases from April 3, 2014 →
Related Congenital cases
- Repaired Tetralogy of Fallot with Left Isomerism, Azygos Continuation of IVC, and Aortic Stenosis
- Foramen of Morgagni Hernia (Incidental)
- Retroesophageal Right Vertebral Artery from Diverticulum of Kommerell (Aortic Arch Variant)
- Circumflex Aorta
- High Origin of the Right Coronary Artery
- Atrial Septal Defect