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Juxtaposed Atrial Appendages with Tetralogy of Fallot and Duplicated SVC

Juxtaposed Atrial Appendages with Tetralogy of Fallot and Duplicated SVC▶ Watch on YouTube — age-restricted, cannot embed here

Imaging findings

A 30-year-old post-repair Tetralogy of Fallot patient presented with duplicated superior vena cava (unconnected by an innominate vein), with the left SVC draining into the coronary sinus. The most striking finding was the absence of a left atrial appendage and the presence of both atrial appendages juxtaposed on the right side in the anterior mediastinum, along with a deep AV groove and a small mitral orifice.

Key takeaways

Juxtaposed atrial appendages, a rare congenital anomaly where both atrial appendages are located on the same side, are typically associated with complex congenital heart disease, particularly situs abnormalities and transposition of the great arteries. This case highlights a rare presentation in conjunction with Tetralogy of Fallot but without other major situs abnormalities, underscoring the spectrum of complex cardiac embryological development.

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