Hypoplastic left heart syndrome with coronary-left atrial fistula
Imaging findings
MRA and cardiac cath in a 2-day-old newborn with hypoplastic left heart syndrome (HLHS) demonstrate a small left ventricle, dilated right heart, large PDA, hypoplastic arch, and a subtle coronary fistula between the left main/LAD coronary artery and the left atrium.
Key takeaways
Coronary arterial fistulas are congenital anomalies that can occur in association with hypoplastic left heart syndrome. They can be very subtle on CTA/MRA and are confirmed by diagnostic cardiac catheterization.
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